Access to society journal content varies across our titles. Pdf file of the complete article 504k, or click on a page image below to browse page by page. A 25 year old male had presented with history of abdominal distension of 20 days duration and on examination he had prominent abdominal vein and a venous hum with ascites. Original article from the new england journal of medicine the cruveilhierbaumgarten syndrome report of a case. Cruveilhierbaumgarten syndrome kruvalya bahmgarten, cirrhosis of the liver with patent umbilical or paraumbilical veins and varicose. At necropsy a widely patent umbilical vein, a small but apparently grossly normal liver, and a. Europe pmc is an elixir core data resource learn more. The pathogenesis of the disease is also briefly discussed. Pegot, in 1833, observed a patient who on examination had dilated, tortuous veins on the abdominal wall with formation of a caput medusae and an audible murmur over the dilated veins on auscultation. Adobe acrobat reader dc software is the free global standard for reliably viewing, printing, and commenting on pdf documents.
The cruveilhierbaumgarten syndrome report of a case nejm. It is the first reported from zambia and from southern africa. The response of the venous hum of the cruveilhierbaumgarten syndrome cbs to respiration, the cardiac cycle, and changes in posture is not predictable. Links to pubmed are also available for selected references. It includes content provided to the pmc international archive by participating publishers. Find out information about cruveilhierbaumgarten sign. Cruveilhier baumgarten syndrome in a cirrhotic patient taking alcohol with boesenbergia pundurata.
Although access to this page is not restricted, the information found here is intended for use by medical providers. Health, general portal hypertension care and treatment diagnosis portal vein medical examination splenomegaly. The cruveilhier baumgarten syndrome portal hypertension associated with compensatory recanalization of the umbilical or paraumbilical veins and a caput medusae. The response of the venous hum of the cruveilhier baumgarten syndrome cbs to respiration, the cardiac cycle, and changes in posture is not predictable. The valsalva maneuver may result in an increase in intensity of the hum rather than a decrease. Cruveilhier baumgarten syndrome with multiple splenic. This results in formation of a network of dilated periumbilical veins medusa head appearance known as cruveilhierbaumgarten syndrome manifesting clinically as abdominal wall bruit the. Full text full text is available as a scanned copy of the original print version. Cruveilhierbaumgarten syndrome in which venous hum. Cruveilhierbaumgarten syndromea caveat for surgeons. Cruveilhierbaumgarten syndrome is a rare syndrome characterised by portal hypertension, splenomegaly and a prominent paraumbilical circulation.
Necropsy by cruveilhier on the same patient in 1852 revealed a small noncirrhotic liver, a large. A case of cruveilhierbaumgarten syndrome is presented, with a discussion of the important clinical features of this entity, which include a prominent paraumbilical vein, a venous hum and a thrill at the site of the paraumbilical circulation, splenomegaly with or without hepatomegaly, anemia, eosinophilia and persistent leukopenia. Cruveilhierbaumgarten murmur definition of cruveilhier. Cruveilhierbaumgarten syndrome the american journal of. And now, its connected to the adobe document cloud. Its the only pdf viewer that can open and interact with all types of pdf content, including. Europe pmc is a service of the europe pmc funders group, in partnership with the european bioinformatics institute. Cruveilhierbaumgarten syndrome definition of cruveilhier. A case of cruveilhierbaumgarten cb disease is described.
Cruveilhierbaumgarten syndrome a caveat for surgeons. A 73yearold woman was hospitalized for treatment of esophageal. It is important to remember that the venous hum of the cruveilhierbaumgarten syndrome may vary from patient to patient and in even the same patient, depending on the collateral circulation involved, the position of the patient, the cardiac output, the presence or absence of ascites, and the cardiac and respiratory. Venous hum of the cruveilhierbaumgarten syndromereply. Case report, report by south african journal of surgery. Get a printable copy pdf file of the complete article 2. Journal of the indian medical association 01 sep 1963, 41. Chicago, illinois in 1833 pegot1 described, in an alcoholic soldier, a slight murmur over subcutaneous abdominal varices. It was first described in 1852 by cruveilhier and then in 1908 by baumgarten. Family practice notebook 2020, family practice notebook, llc. Cruveilhier baumgarten syndrome is an uncommon condition with very few cases reported in literature. Adobe acrobat reader dc download free pdf viewer for. It is a rare medical condition with distension of umbilical or paraumbilical veins, characterized by the presence of an abdominal wall bruit and a. Patients should address specific medical concerns with their physicians.
1078 1290 1025 979 1071 297 1431 1070 545 133 1036 1254 1151 551 1346 236 1552 1291 66 28 205 1539 268 214 719 1347 535 1346 602 1089 457 1619 1492 1236 602 1431 251 850 836 1131 569 1248 1032